EC Paediatrics

Congenital pulmonary adenomatoid malformation (CPAM) is an infrequent developing lung abnormality. We document the case of a 14-day-old term infant who had escalating respiratory distress, repeated pneumothoraxes, and substantial pleural effusion before being diagnosed with bilateral CPAM with superimposed infection. The case exemplifies the diagnostic obstacles given by CPAM when masked by acute respiratory disease and the significance of sophisticated imaging and interdisciplinary care in such complex patients.

 Keywords: Cystic Adenomatoid Malformation Of Lung; Congenital; Neonate; Pneumothorax; Pleural Effusion; Respiration

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