EC Paediatrics

The majority of pediatric brain tumors originate within the posterior fossa, most commonly including juvenile pilocytic astrocytomas, medulloblastomas (MB), ependymomas, and brainstem gliomas. This report describes the case of a 10-year-old patient with underlying hereditary microspherocytosis presenting with headaches, vomiting, and a cerebellar syndrome. Brain computed tomography (CT) and brain magnetic resonance imaging (MRI) with magnetic resonance spectroscopy (MRS), displaying classic features, revealed a well-circumscribed dual cystic-solid lesion of the medulla oblongata without obstructive hydrocephalus. Pilocytic astrocytoma, ganglioglioma, ependymoma, and hemangioblastoma are among the main differential diagnoses.

Keywords: Pilocytic Astrocytoma; Brainstem; Cerebellar Syndrome; MRI; Magnetic Resonance Spectroscopy; Child

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