EC Paediatrics

Acinic cell carcinoma (ACC) is a rare malignant epithelial tumor of the salivary glands, accounting for only 2-5% of all primary parotid neoplasms. Although typically seen in adults with a slight female predominance, its occurrence in children is extremely rare. ACC is considered a low-grade malignancy, often displaying well-differentiated histological features that resemble normal acinar cells of the salivary gland. Radiologically, these tumors often appear well-circumscribed and encapsulated, which can mimic benign lesions such as pleomorphic adenomas, making preoperative diagnosis challenging. In pediatric patients, this resemblance may delay suspicion of malignancy. Therefore, histopathological examination remains essential for a definitive diagnosis and for guiding appropriate management.

 Keywords: Acinic Cell Carcinoma; Pediatric Parotid Tumor; Salivary Gland Neoplasm

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