EC Paediatrics

Gaucher's disease is an uncommon disorder which has been reported to be associated with an increased risk of lymphoproliferative disorders, including Hodgkin's lymphoma (A new instance of such an association is described here. This was a 13 year-old-patient with a type I Gaucher's disease who, after 11 years after the above diagnosis, presented with lymphadenopathy of the level of chain VI, This led to the diagnosis of large-cell Hodgkin lymphoma successfully treated with chemotherapy.

 Keywords: Hodgkin; Gaucher Disease; Pediatric; Genetic Disorder

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