EC Paediatrics

Biliary atresia classically presents at neonatal age, late presentation in infancy is very rare. We discuss the challenges in clinical diagnosis and henceforth its management, unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery with timely referrals. Here we highlight the importance of considering biliary atresia as one of rare differentials in infants with cholestasis syndromes. We present late-onset biliary atresia in a 19 weeks old baby presenting with jaundice. This article highlights late-onset case BA, showcasing importance of BA as differential diagnosis not just in neonates, but also in infants with cholestatic syndrome. Babies should be evaluated by physicians be it a GP, pediatrician or a gastroenterologist based on clinical, laboratory, histopathological, and imaging criteria. BA could be challenging to diagnose but a timely referral and surgical intervention can improve prognosis and survival.
Keywords: Biliary Atresia; Jaundice; Cholestasis Syndromes

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