EC Orthopaedics

Objective: To evaluate the clinical and functional outcomes of a technical procedure used in the surgical treatment of congenital constriction rings (CCR) in children.

Materials and Methods: This is a retrospective study conducted to evaluate the outcomes of surgical techniques performed between January 1995 and December 2022 on 127 patients with 185 congenital constrictions. The patient group included 68 female infants and 59 male infants.

The degree of constriction was classified according to the Patterson criteria, with a median age at surgery of 1 year 10 months (range 4 days to 4 years 5 months).

Results: Three types of CCR (Patterson criteria) were identified among 127 patients (185 loops): type I (8 patients, 4.3%), type II (163, 88.1%), type III (14, 7.6%). The mean follow-up period was 7 years and 9 months (range, 2 years and 9 months to 15 years and 7 months). The surgical results according to Moses criteria [14] of 185 loops, good results were achieved in 73.5% and fair results in 26.5%. Six patients presented with sensory disturbances immediately after surgery but all six patients improved to normal condition at the final follow-up. There were no skin necrosis or wound healing problems.

Conclusion: The combined sinuplasty/fibular resection and fasciotomy reported here is a simple and safe surgical technique for the treatment of congenital loop constriction syndrome in children.

 Keywords: Congenital Constriction Syndrome; Fat Flap; Amniotic Ring; Direct Closure; Z-Plasty

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