EC Neurology

En plaque meningioma is a rare subtype of meningioma characterized by sheet-like growth, infiltrative behavior, and frequent hyperostosis, often affecting the orbit and skull base. A 55-year-old man presented with right-sided proptosis and headache. MRI demonstrated a dural-based right spheno-orbital lesion infiltrating orbital fat and temporalis muscle, with associated spheno-orbital hyperostosis. Subtotal resection with bony decompression of the superior orbital fissure and optic canal was performed, followed by adjuvant radiotherapy due to the tumor’s infiltrative nature and extension into critical structures. At 3-year follow-up, MRI revealed no recurrence, and the patient achieved favorable functional and cosmetic outcomes. En plaque meningiomas are surgically challenging, but multimodal management combining surgery and radiotherapy can provide durable disease control with satisfactory outcomes.

 Keywords: En Plaque Meningioma; Exophthalmos; Sphenoid Wing; MRI

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