EC Ophthalmology

Introduction: Neurofibroma is a benign nodular nerve tumor. It may be isolated or associated with neurofibromatosis. Orbital neurofibromas may be associated with lesions of the eyelids, conjunctiva, uvea, sclera and episclera.

Medical Observation: We report the case of a 36-year-old patient who presented with a right superior-internal palpebral swelling that had been evolving for 6 years, with an increase in volume and exophthalmos for one year. The oculo-orbito-palpebral examination revealed preserved right visual acuity of 10/10, a non-axial, painless, irreducible right exophthalmos measuring 23 mm on the Hertel, and a nodular right superior-internal palpebral mass, adherent to the deep plane, painless and with clear contours. An orbito-cerebral CT scan isolated a polylobed right intra-orbital, extra-ocular superior and medial mass measuring 38 mm× 30 mm in axial height, coming into contact with the thickened superior rectus muscle without bony lesions at its contact, in favour of a cystic tumour. An anterior orbitotomy was performed, with excision of the mass in toto. Pathological analysis was in favor of a neurofibroma. Progression was favourable.

Conclusion: Neurofibromas are rare and benign in origin, and surgical removal is for functional and/or cosmetic purposes.

 Keywords: Intraorbital Mass; Exophthalmos; Anterior Orbitotomy; Benign Tumor

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