EC Ophthalmology

Introduction: Optic disc edema and/or vascular tortuosity associated with Kawasaki disease (KD) have been rarely described. We, therefore, reported four cases with optic disc swelling and retinal vascular tortuosity associated with KD identified in early fundoscopy exam in children with remarkable conjunctival injection.

Case Reports: The median age at KD diagnosis was 3.25 years (range 2.42 - 5.5). All patients fulfilled the EULAR/PReS criteria for KD, with bilateral bulbar nonexudative conjunctivitis. Ophthalmological examination (Slit-lamp biomicroscopy, ophthalmoscopy and visual acuity) revealed: four patients had bilateral optic disc swelling and two presented bilateral retinal vascular tortuosity. All KD patients received intravenous immunoglobulin and acetylsalicylic acid, with total improvement of ophthalmological abnormalities in up to two months.

Discussion: We observed herein posterior eye segment involvement resulting in bilateral optic disc swelling and retinal tortuosity in KD patients with marked conjunctivitis during acute febrile phase. Prompt KD treatment suggested good outcome for these ophthalmological abnormalities.

 Keywords: Kawasaki Disease; Ocular; Eye; Optic Disc Edema and Children

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