EC Gynaecology

Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital Müllerian anomaly characterized by uterus didelphys, hemivaginal septum, and unilateral renal agenesis. This case involves a 14-year-old girl exhibiting all features of the syndrome who presented with a lower abdominal mass. Despite its rarity, preoperative diagnosis is possible with a strong clinical suspicion and an MRI scan, which is considered the gold standard for diagnosis. Early diagnosis is crucial to prevent complications associated with delayed diagnosis.

 Keywords: Congenital Mullerian Anomaly; Renal Agenesis; Haematocolpos

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