EC Gastroenterology and Digestive System

Isolated polycystic liver disease is a rare disease. Patients with isolated polycystic liver disease are usually asymptomatic and the liver cysts are detected incidentally on imaging studies performed for other purposes. Patients rarely develop symptoms, which are most often secondary to cyst enlargement and hepatomegaly. Management of symptomatic PCLD focuses on symptom relief and treatment of complications.

We report the case of a 39-year-old man who presented with ascites and febrile jaundice, whose laboratory tests showed an infectious syndrome, cholestasis and negative hydatid and viral serologies. The CT scan showed a hepatomegaly with multiple cysts of variable size, ascites and normal kidney structure. The diagnosis of isolated polycystic hepatitis was retained. The patient was put on antiobiotherapy with albumin infusion, the patient's clinical and biological condition has improved evolution.

 Keywords: Isolated Polycystic Liver Disease; Jaundice; Ascites; Infectious Hepatic Cyst

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