EC Dental Science

Case Report Volume 23 Issue 10 - 2024

Aggressive Fibromatosis in Lower Body of Mandible: A Rare Entity Report of a Case

Hina Handa1*, Shweta Chaturvedi2 and Kavita Badi3

1Professor, Oral Medicine and Radiology, People’s Dental Academy, People’s University, Bhopal, India
2Reader, Oral Medicine and Radiology, People’s Dental Academy, People’s University, Bhopal, India
3Senior Lecturer, Oral Medicine and Radiology, People’s Dental Academy, People’s University, Bhopal, India

*Corresponding Author: Hina Handa, Professor, Oral Medicine and Radiology, People’s Dental Academy, People’s University, Bhopal, India.
Received: August 12, 2024; Published: September 24, 2024



The fibromatosis are a rare group of lesions that can infiltrate widely, replacing muscle, fat and bone with fibrous tissue of varying cellularity. They do not develop distant metastases, however, locally they show an aggressive and infiltrative behaviour. Clinically, aggressive fibromatosis manifests as a painless, firm, often rapidly enlarging mass, fixed to underlying bone or soft tissue. It is never encapsulated. Histologically, it is rich in collagen and fibroblastic cells that are devoid of hyperchromatic or atypical nuclei. Treatment is based on either excision of the mass, or radiotherapy and chemotherapy if the condition is inoperable. We describe a case of aggressive fibromatosis of the mandible in a young adult initially misdiagnosed as a case of some centrally originated pathology.

Keywords: Fibromatosis; Fibromatosis Mandible; Desmoid Tumor

 

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Hina Handa., et al. “Aggressive Fibromatosis in Lower Body of Mandible: A Rare Entity Report of a Case”.”. EC Dental Science 23.10 (2024): 01-06.