EC Dental Science

The fibromatosis are a rare group of lesions that can infiltrate widely, replacing muscle, fat and bone with fibrous tissue of varying cellularity. They do not develop distant metastases, however, locally they show an aggressive and infiltrative behaviour. Clinically, aggressive fibromatosis manifests as a painless, firm, often rapidly enlarging mass, fixed to underlying bone or soft tissue. It is never encapsulated. Histologically, it is rich in collagen and fibroblastic cells that are devoid of hyperchromatic or atypical nuclei. Treatment is based on either excision of the mass, or radiotherapy and chemotherapy if the condition is inoperable. We describe a case of aggressive fibromatosis of the mandible in a young adult initially misdiagnosed as a case of some centrally originated pathology.

Keywords: Fibromatosis; Fibromatosis Mandible; Desmoid Tumor

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