EC Clinical and Medical Case Reports

Introduction: Solid pseudo-papillary tumors of the pancreas (SPT) described in 1959 by Dr. Frantz, are tumors with low malignancy potential, representing 1 - 2% of exocrine tumors of the pancreas. They mainly effect young women [1,2]. They are characterized by atypical symptomatology, ranging from a simple gene to signs of compression or invasion of the pancreas or pancreatic duct, sometimes even revealing metastases or fortuitous discovery during imaging [3-6]. Surgical resection remains the only treatment for SPT. The type and extent of this resection depends on the location of the pancreas, size, and extent of the tumor. The prognosis is generally favorable with a long life without recurrence [2]. In this article, we report a case of a patient with a large SPT of the head of the pancreas that was surgically treated with a cephalic duodeno-pancreatectomy (CDP).

Observation: We report the case of a young woman operated for a pseudopapillary tumor of the head of the pancreas discovered incidentally during an ultrasound. The echoendoscopy (EE) in addition to the characteristics of the tumor allowed the realization of a puncture-biopsy; the histopathological study was in favor of a SPT of the pancreas. The patient underwent cephalic pancreaticoduodenectomy according to Whipple. The postoperative follow-up was simple except for a grade B pancreatic fistula.

Conclusion: Solid pseudo-papillary tumors of the pancreas are rare tumors. Treatment is surgical. Recurrences are rare and late, hence the need for long-term follow-up.

Keywords: SPT of the Pancreas; Surgery; Recurrence; Pancreatic Fistula

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