EC Clinical and Medical Case Reports

Low-grade fibromyxoid sarcoma also known as Evans tumor, is a rare soft tissue tumor that can occur in all parts of the soft tissues, especially in the deep soft tissues, generally localizes to the extremities and trunk, the primary intra thoracic location is uncommon.

Although the histological appearance is benign, the risk of recurrence and metastases is high, requiring long-term monitoring.

We report the case of a 29-year-old woman presenting with pleural fibromyxoid sarcoma, which is an exceptional primary site of development, associated with pulmonary metastases.

 Keywords: Evans Tumor; Immunohistochemistry; CT Scan

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