EC Clinical and Medical Case Reports

Primary leiomyosarcoma of the inferior cava vena is an exceptionally rare malignant tumor arising from the smooth muscle of the vessel wall, with only a few hundred cases that have been documented in medical literature. There are no well-defined treatment protocols; however, surgical removal currently stands as the sole curative option. Further research is essential to gain a deeper understanding of the disease and provide guidance for its management. We present a case involving a 50-year-old man who was admitted with a six-month history of vague abdominal pain and weight loss. Abdominal computed tomography revealed a mass araising from with the inferior vena cava associated with hepatic nodules. Histological examination confirmed the diagnosis of leiomyosarcoma of the inferior vena cava with liver metastases.

 Keywords: Leiomyosarcoma; Liver; Primary; Imaging; Inferior Vena Cava

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