EC Clinical and Medical Case Reports

Research Article Volume 7 Issue 2 - 2024

Negative Rectoanal Inhibitory Reflex in Anorectal Manometry...It is Not Always Hirschsprung's Disease

Fernandez J1, Oviedo A1, Messere G1, Ortiz G1, Breden X2, Berger M2 and Bigliardi Román1*

1Servicio de Gastroenterología Pediátrica, Hospital Nacional Profesor Alejandro Posadas, Buenos Aires, Argentina

2Servicio de Cirugía Infantil, Hospital Nacional Profesor Alejandro Posadas, Buenos Aires, Argentina

*Corresponding Author: Bigliardi Román, Servicio de Gastroenterología Pediátrica, Hospital Nacional Profesor Alejandro Posadas, Buenos Aires, Argentina.
Received: January 03, 2024; Published: January 29, 2024



This study, conducted between June 2005 and June 2021, aimed to determine the presence of the rectoanal inhibitory reflex (RAIR) in patients with Anorectal Malformations (ARM) and its relationship with the height of the ARM. The study involved 63 patients aged 6 to 17 years who had undergone surgery for ARM using the Peña technique. The results showed that the RAIR was not found in 27% of the patients. Height of the ARM was significant in determining RAIR presence, being more frequent in patients with low lesions. The study also found higher frequency of rectosphincteric dyssynergia in high malformations than in low ones, which was statistically significant. The study concluded that the absence of RAIR is not always due to the presence of Hirschsprung's Disease (HD) and that taking a biopsy is not mandatory in all cases.

 Keywords: Anorectal Malformations; Child; Anorectal Manometry; Fecal Incontinence

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Bigliardi Román., et al. "Negative Rectoanal Inhibitory Reflex in Anorectal Manometry...It is Not Always Hirschsprung's Disease." EC Clinical and Medical Case Reports   7.2 (2024): 01-07.