EC Clinical and Medical Case Reports

Chronic thromboembolic pulmonary hypertension (CTEHP) according to the European Guidelines for the diagnosis and treatment of pulmonary hypertension (PH) is classified in the fourth group. CTEPH is a rare, but progressive and potentially life-threatening condition that most commonly occurs due to pulmonary artery obstruction from unresolved acute pulmonary embolism (PE). There are different data on the occurrence of CTEPH after acute PE, which is primarily due to the different factors of occurrence, sometimes due to non-specificity of symptoms and the difficulty in differentiating acute pulmonary embolism from the symptoms of pre-existing CTEPH. We present a patient with CTEPH with recurrent episodes of acute pulmonary embolism, as the cause of development of right heart failure and poor outcome.

Keywords: Pulmonary Embolism; Pulmonary Hypertension; Chronic Thromboembolic Pulmonary Hypertension; Thrombophilia; Right Heart Failure; Dyspnea

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