EC Clinical and Medical Case Reports

Behçet's syndrome (BS) is a multisystem inflammatory disorder of unknown etiology, characterized by recurrent oral ulcers, genital ulcers, and uveitis. This condition, which shows a particular prevalence in countries along the Silk Road, including Turkey, where the incidence is highest, represents a significant challenge in terms of diagnosis and management. The syndrome may also involve various organ systems, leading to a wide range of clinical manifestations. Here, we discuss the case of a patient presenting with multiple pulmonary artery aneurysms (PAAs), a rare but severe complication of BS. The discussion focuses on the diagnostic process, therapeutic options, and the importance of a multidisciplinary approach in managing such complex cases.

 Keywords: Silk Road; Pulmonary Artery Aneurysms (PAAs); Behçet's Disease

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