EC Clinical and Medical Case Reports

Dandy-walker syndrome is characterized by hypoplasia of cerebellar vermis and cystic enlargement of the fourth ventricle.

Majority of patients present with hydrocephalus which may be associated with atresia of the foramen of magendie.

Approximately 70% - 90% of patients have hydrocephalus. It may be associated with atresia of the foramen of magendie and possibly, the foramen of Luschka. Dandy walker syndrome occurs in one out of every 25,000 live births, occurs more frequently in females than males [1].

This report presents DWS in a 40 day old baby boy.

 Keywords: Dandy Walker Syndrome [DWS]; Hydrocephalus

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